Chiari Malformations


  • Chiari malformation is an abnormality of the anatomy at the bottom of the skull and brain leading to neurological symptoms.
  • There are 4 types of chiari malformations:  Chiari type 1, 2, 3 and 4.
  • Chiari type 2 is a developmental malformation that leads to myelomeningocele (incomplete closure of the back and spinal cord), hydrocephalus (too much cerebral spinal fluid in the brain), and brain abnormalities. These are often operated on at birth or soon after. 
  • Chiari type 3 and 4 are not compatible with life.
  • This page will cover Chiari Malformation type 1.